A 60-year-old woman with tricuspid atresia had previously undergone palliation with a Glenn procedure and a Blalock-Taussig shunt, and finally correction with a Fontan procedure. Twenty-five years later, severe atrioventricular valve regurgitation with concomitant valvular prolapse and cleft leading to heart failure was successfully treated using 1 single MitraClip XTW, confirming its effectiveness as a lower-risk alternative to surgery. The patient showed marked improvement of heart failure–related symptoms, with residual mild to moderate regurgitation and improved liver function.

Percutaneous Atrioventricular Valve Repair With MitraClip in Failed Adult Fontan Circulation for Tricuspid Atresia / Testerini, F. B. B.; Gramegna, F.; Denti, P.; Bragato, R. M.; Agricola, E.; Presbitero, P.; Condorelli, G.; Maisano, F.. - In: JACC. CASE REPORTS. - ISSN 2666-0849. - 30:9(2025). [10.1016/j.jaccas.2025.103272]

Percutaneous Atrioventricular Valve Repair With MitraClip in Failed Adult Fontan Circulation for Tricuspid Atresia

Gramegna F.;Agricola E.;Maisano F.
2025-01-01

Abstract

A 60-year-old woman with tricuspid atresia had previously undergone palliation with a Glenn procedure and a Blalock-Taussig shunt, and finally correction with a Fontan procedure. Twenty-five years later, severe atrioventricular valve regurgitation with concomitant valvular prolapse and cleft leading to heart failure was successfully treated using 1 single MitraClip XTW, confirming its effectiveness as a lower-risk alternative to surgery. The patient showed marked improvement of heart failure–related symptoms, with residual mild to moderate regurgitation and improved liver function.
2025
congenital heart disease
Fontan circulation
MitraClip
transcatheter-based treatments
tricuspid atresia
univentricular heart
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Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/20.500.11768/182939
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