Herein we describe the occurrence of an acquired torpedo-like maculopathy in a patient with genetically confirmed BEST1-associated vitelliform macular dystrophy. Multimodal imaging suggests limited exudation from subclinical macular neovascularization as a potential trigger, promoting local fluorophore accumulation and lesion development on a background of chronic retinal pigment epithelium dysfunction.

ACQUIRED TORPEDO-LIKE MACULOPATHY ASSOCIATED WITH MACULAR NEOVASCULARIZATION IN BEST VITELLIFORM MACULAR DYSTROPHY / Parodi, M. B.; Bianco, L.; Antropoli, A.; Nunziata, A.; Del Fabbro, S.; Arrigo, A.; Bandello, F.. - In: RETINA. - ISSN 0275-004X. - (2025). [10.1097/IAE.0000000000004666]

ACQUIRED TORPEDO-LIKE MACULOPATHY ASSOCIATED WITH MACULAR NEOVASCULARIZATION IN BEST VITELLIFORM MACULAR DYSTROPHY

Parodi M. B.
Primo
;
Bianco L.;Antropoli A.;Nunziata A.;Del Fabbro S.;Arrigo A.;Bandello F.
Ultimo
2025-01-01

Abstract

Herein we describe the occurrence of an acquired torpedo-like maculopathy in a patient with genetically confirmed BEST1-associated vitelliform macular dystrophy. Multimodal imaging suggests limited exudation from subclinical macular neovascularization as a potential trigger, promoting local fluorophore accumulation and lesion development on a background of chronic retinal pigment epithelium dysfunction.
2025
Best vitelliform macular dystrophy
BEST1
macular neovascularization
OCT angiography
torpedo
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Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/20.500.11768/200480
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